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Course Description

High-yield biochemistry and genetics review for USMLE Step 1. Covers metabolic pathways, enzyme deficiencies, genetic disorders, molecular biology, and laboratory diagnostics. Emphasis on clinical correlations and pattern recognition for vignette-based questions.

Learning Objectives

  • Explain major metabolic pathways and their regulation
  • Identify enzyme deficiencies from clinical presentations
  • Apply principles of molecular genetics to disease mechanisms
  • Interpret laboratory findings in metabolic disorders
  • Recognize inheritance patterns and calculate genetic risks

Topics

  • Amino Acid Metabolism: PKU, maple syrup urine disease, homocystinuria
  • Carbohydrate Metabolism: Glycogen storage diseases, galactosemia
  • Lipid Metabolism: Lipid storage diseases, hyperlipidemia
  • Purine and Pyrimidine Metabolism: Gout, Lesch-Nyhan
  • DNA Replication, Transcription, Translation
  • Genetic Disorders: Chromosomal, Mendelian, Mitochondrial
  • Molecular Techniques: PCR, blotting, sequencing

Materials

  • 20 hours of video lectures
  • 300+ practice questions
  • Metabolic pathway diagrams
  • Genetic pedigree analysis exercises
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